Clinical case: abdominal wall malformation?

[Stefan Johansson]

Dear all,
I have been asked to post the following clinical case born in a Swedish hospital:
Term infant, normal pregnancy and delivery.
The infant has a "ridge" of umbilical-like tissue, stretching from the umbilicus and to sternal tip. The ridge is freely movable from the deeper structure. No secretion. There are no external malformation apart from this ridge. The infant is well, breast-feeding normally, has passed meconium and urine, not vomiting etc.
A plain abdominal x-ray has shown no pathologies.

It seems that the infant has some kind of abdominal wall defekt, but what is the diagnosis? Has anyone seen something similar?

http://99nicu.org/images2/abd_wall1.jpg

http://99nicu.org/images2/abd_wall2.jpg

[Stefan Johansson]

Some feedback:
an incomplete and mild form of Pentalogy of Cantrell seems the main differential diagnosis.
This infant has no serious internal malformations, such as cardiac malformation, diaphr hernia etc., and is doing fine.

The pentalogy of Cantrell is a very rare disorder/syndrome characterized by a combination of severe defects of the middle of the chest including the sternum, diaphragm, heart, and abdominal wall. This defect can affect males or females and is apparent at birth or shortly after.

[Mariam]

This is interesting. this is the first time I see such a case

[galaxy_7]

we had a similar case about 2 years ago and turned to be some kind of hemangioma and our vascular surgeon operated on it .. u must search for other hidden visceral hemangiomas

thanx
emad